Nutrition and metabolic disorders | |||||
---|---|---|---|---|---|
Nutrition and metabolic disorders / Metabolic acidosis | |||||
trometamol | Hospital Only | ||||
Solution for infusion | |||||
Trometamol (Non-proprietary) | Hospital Only | ||||
Nutrition and metabolic disorders / Vitamin deficiency | |||||
alfacalcidol | Hospital Only | ||||
Oral drops | |||||
One-Alpha (Neon Healthcare Ltd) | Hospital Only | ||||
Solution for injection | |||||
One-Alpha (Neon Healthcare Ltd) | Hospital Only | ||||
alpha tocopherol | Amber | ||||
Oral solution | |||||
Vedrop (Recordati Rare Diseases UK Ltd) | Amber | ||||
alpha tocopheryl acetate | Amber | ||||
Oral suspension | |||||
Alpha tocopheryl acetate (Non-proprietary) | Amber | ||||
Solution for injection | |||||
Alpha tocopheryl acetate (Non-proprietary) | Hospital Only | ||||
ascorbic acid | Amber | ||||
Chewable tablet | |||||
Ascorbic acid (Non-proprietary) | Amber | ||||
biotin | Hospital Only | ||||
Solution for injection | |||||
Biotin (Non-proprietary) | Hospital Only | ||||
calcitriol | Hospital Only | ||||
Oral solution | |||||
Calcitriol (Non-proprietary) | Hospital Only | ||||
colecalciferol | Amber | ||||
Chewable tablet | |||||
Colecalciferol (Non-proprietary) | Non-Formulary | ||||
Orodispersible tablet | |||||
Colecalciferol (Non-proprietary) | Non-Formulary | ||||
Oral solution | |||||
Colecalciferol (Non-proprietary) | Non-Formulary | ||||
Aciferol D3 (Rhodes Pharma Ltd) | Amber | ||||
InVita D3 (Consilient Health Ltd) | Amber | ||||
SunVit D3 (SunVit-D3 Ltd) | Amber | ||||
Thorens (Galen Ltd) | Amber | ||||
Oral drops | |||||
Colecalciferol (Non-proprietary) | Non-Formulary | ||||
Fultium-D3 (Internis Pharmaceuticals Ltd) | Amber | ||||
InVita D3 (Consilient Health Ltd) | Amber | ||||
Pro D3 (Synergy Biologics Ltd) | Amber | ||||
SunVit D3 (SunVit-D3 Ltd) | Amber | ||||
Thorens (Galen Ltd) | Amber | ||||
ergocalciferol | Non-Formulary | ||||
Oral solution | |||||
Ergocalciferol (Non-proprietary) | Non-Formulary | ||||
Eciferol (Rhodes Pharma Ltd) | Non-Formulary | ||||
Solution for injection | |||||
Ergocalciferol (Non-proprietary) | Non-Formulary | ||||
menadiol sodium phosphate | Amber | ||||
phytomenadione | Amber | ||||
pyridoxine hydrochloride | Amber | ||||
Solution for injection | |||||
Pyridoxine hydrochloride (Non-proprietary) | Hospital Only | ||||
riboflavin | Amber | ||||
thiamine | Amber | ||||
Solution for injection | |||||
Thiamine (Non-proprietary) | Hospital Only | ||||
vitamin A | Non-Formulary | ||||
Oral drops | |||||
Vitamin A (Non-proprietary) | Non-Formulary | ||||
Solution for injection | |||||
Vitamin A (Non-proprietary) | Hospital Only | ||||
vitamin B complex | Non-Formulary | ||||
Oral solution | |||||
Vigranon-B (Wallace Manufacturing Chemists Ltd) | Non-Formulary | ||||
vitamins A and D | Non-Formulary | ||||
vitamins with minerals and trace elements | |||||
Oral emulsion | |||||
Vitamins with minerals and trace elements (Non-proprietary) | Amber | ||||
Nutrition and metabolic disorders / Neural tube defects (prevention in pregnancy) | |||||
folic acid | Formulary | ||||
Oral solution | |||||
Folic acid (Non-proprietary) | Formulary | ||||
Lexpec (Rosemont Pharmaceuticals Ltd) | Formulary | ||||
Nutrition and metabolic disorders / Zinc deficiency | |||||
zinc sulfate | Amber | ||||
Nutrition and metabolic disorders / Fluid and electrolyte imbalances | |||||
disodium hydrogen citrate with glucose, potassium chloride and sodium chloride | Formulary | ||||
glucose | Hospital Only | ||||
Infusion | |||||
Glucose (Non-proprietary) | Hospital Only | ||||
Solution for infusion | |||||
Glucose (Non-proprietary) | Hospital Only | ||||
potassium chloride with potassium bicarbonate | Amber | ||||
sodium bicarbonate | Amber | ||||
Oral solution | |||||
Sodium bicarbonate (Non-proprietary) | Amber | ||||
Solution for injection | |||||
Sodium bicarbonate (Non-proprietary) | Hospital Only | ||||
Infusion | |||||
Sodium bicarbonate (Non-proprietary) | Hospital Only | ||||
sodium chloride | Amber | ||||
Modified-release tablet | |||||
Slow Sodium (Alturix Ltd) | Amber | ||||
Solution for injection | |||||
Sodium chloride (Non-proprietary) | Hospital Only | ||||
Infusion | |||||
Sodium chloride (Non-proprietary) | Hospital Only | ||||
Solution for infusion | |||||
Sodium chloride (Non-proprietary) | Hospital Only | ||||
Nutrition and metabolic disorders / Low blood volume | |||||
albumin solution | Hospital Only | ||||
Solution for infusion | |||||
Albumin solution (Non-proprietary) | Hospital Only | ||||
Albunorm (Octapharma Ltd) | Hospital Only | ||||
Alburex (CSL Behring UK Ltd) | Hospital Only | ||||
Zenalb (Bio Products Laboratory Ltd) | Hospital Only | ||||
gelatin | Hospital Only | ||||
Infusion | |||||
Gelaspan (B.Braun Medical Ltd) | Hospital Only | ||||
Gelofusine (B.Braun Medical Ltd) | Hospital Only | ||||
Geloplasma (Fresenius Kabi Ltd) | Hospital Only | ||||
Isoplex (Kent Pharma (UK) Ltd) | Hospital Only | ||||
Volplex (Kent Pharma (UK) Ltd) | Hospital Only | ||||
Nutrition and metabolic disorders / Hyperphosphataemia | |||||
sevelamer | Hospital Only | ||||
Nutrition and metabolic disorders / Hypophosphataemia | |||||
phosphate | Amber | ||||
Infusion | |||||
Phosphate (Non-proprietary) | Hospital Only | ||||
Solution for infusion | |||||
Phosphate (Non-proprietary) | Hospital Only | ||||
Nutrition and metabolic disorders / Hyperkalaemia | |||||
calcium polystyrene sulfonate | Hospital Only | ||||
insulin | Hospital Only |
NICE TA151 NICE TA943 |
|||
Solution for injection | |||||
Insulin (Non-proprietary) | Hospital Only | ||||
Actrapid (Novo Nordisk Ltd) | Hospital Only | ||||
Humulin S (Eli Lilly and Company Ltd) | Hospital Only | ||||
Hypurin Porcine Neutral (Wockhardt UK Ltd) | Hospital Only | ||||
sodium polystyrene sulfonate | Hospital Only | ||||
Nutrition and metabolic disorders / Hypokalaemia | |||||
potassium chloride | Amber | ||||
Modified-release tablet | |||||
Potassium chloride (Non-proprietary) | Non-Formulary | ||||
Oral solution | |||||
Kay-Cee-L (Geistlich Sons Ltd) | Amber | ||||
Solution for infusion | |||||
Potassium chloride (Non-proprietary) | Hospital Only | ||||
Nutrition and metabolic disorders / Hypomagnesaemia | |||||
magnesium aspartate | Amber | ||||
magnesium glycerophosphate | Amber | ||||
Chewable tablet | |||||
Magnesium glycerophosphate (Non-proprietary) | Non-Formulary | ||||
magnesium sulfate | Hospital Only | ||||
Solution for injection | |||||
Magnesium sulfate (Non-proprietary) | Hospital Only | ||||
Solution for infusion | |||||
Magnesium sulfate (Non-proprietary) | Hospital Only | ||||
Nutrition and metabolic disorders / Nutrition (intravenous) | |||||
parenteral nutrition supplements | Hospital Only | ||||
Solution for infusion | |||||
Parenteral nutrition supplements (Non-proprietary) | Hospital Only | ||||
Dipeptiven (Fresenius Kabi Ltd) | Hospital Only | ||||
Peditrace (Fresenius Kabi Ltd) | Hospital Only | ||||
Tracutil (B.Braun Medical Ltd) | Hospital Only | ||||
Nutrition and metabolic disorders / Tyrosinaemia type I | |||||
nitisinone | Hospital Only | ||||
Oral suspension | |||||
Orfadin (Swedish Orphan Biovitrum Ltd) | Hospital Only | ||||
Nutrition and metabolic disorders / Mucopolysaccharidosis | |||||
galsulfase | Hospital Only | ||||
Solution for infusion | |||||
Naglazyme (BioMarin (U.K.) Ltd) | Hospital Only | ||||
idursulfase | Hospital Only | ||||
Solution for infusion | |||||
Elaprase (Takeda UK Ltd) | Hospital Only | ||||
laronidase | Hospital Only | ||||
Solution for infusion | |||||
Aldurazyme (Sanofi) | Hospital Only | ||||
Nutrition and metabolic disorders / Gaucher's disease | |||||
imiglucerase | Hospital Only | ||||
miglustat | Hospital Only | ||||
velaglucerase alfa | Hospital Only | ||||
Nutrition and metabolic disorders / Niemann-Pick disease | |||||
miglustat | Hospital Only | ||||
Nutrition and metabolic disorders / Acute porphyrias | |||||
haem arginate | Hospital Only | ||||
Solution for infusion | |||||
Normosang (Recordati Rare Diseases UK Ltd) | Hospital Only | ||||
Nutrition and metabolic disorders / Carnitine deficiency | |||||
levocarnitine | Hospital Only | ||||
Oral solution | |||||
Levocarnitine (Non-proprietary) | Hospital Only | ||||
Nutrition and metabolic disorders / Cystinuria | |||||
penicillamine | Hospital Only | ||||
Nutrition and metabolic disorders / Wilson's disease | |||||
penicillamine | Hospital Only | ||||
trientine | Hospital Only | ||||
zinc acetate | Hospital Only | ||||
Nutrition and metabolic disorders / Fabry's disease | |||||
agalsidase alfa | Hospital Only | ||||
Solution for infusion | |||||
Replagal (Takeda UK Ltd) | Hospital Only | ||||
agalsidase beta | Hospital Only | ||||
Nutrition and metabolic disorders / Pompe disease | |||||
alglucosidase alfa | Hospital Only | ||||
Nutrition and metabolic disorders / Homocystinuria | |||||
betaine | Hospital Only | ||||
Nutrition and metabolic disorders / Mitochondrial disorders | |||||
ubidecarenone | Hospital Only | ||||
Chewable tablet | |||||
Ubidecarenone (Non-proprietary) | Hospital Only | ||||
Oral drops | |||||
Ubidecarenone (Non-proprietary) | Hospital Only | ||||
Nutrition and metabolic disorders / Urea cycle disorders | |||||
arginine | Hospital Only | ||||
Solution for infusion | |||||
Arginine (Non-proprietary) | Hospital Only | ||||
Form unstated | |||||
Arginine (Non-proprietary) | Hospital Only | ||||
carglumic acid | Hospital Only | ||||
citrulline | Hospital Only | ||||
Form unstated | |||||
Citrulline (Non-proprietary) | Hospital Only | ||||
sodium benzoate | Hospital Only | ||||
sodium dichloroacetate | Hospital Only | ||||
sodium phenylbutyrate | Hospital Only | ||||
Nutrition and metabolic disorders / Nephropathic cystinosis | |||||
mercaptamine | Hospital Only | ||||
Nutrition and metabolic disorders / Hypophosphatasia | |||||
asfotase alfa | Hospital Only |
NICE HST23 |
|||
Solution for injection | |||||
Strensiq (Alexion Pharma UK Ltd) | Hospital Only | ||||
Nutrition and metabolic disorders / Phenylketonuria | |||||
sapropterin dihydrochloride | Hospital Only |
NICE TA729 |