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Nutrition and metabolic disorders
Nutrition and metabolic disorders / Metabolic acidosis
  trometamol HOSPITAL ONLY PRESCRIBING
  Solution for infusion
Trometamol (Non-proprietary) HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Vitamin deficiency
  alfacalcidol HOSPITAL ONLY PRESCRIBING
  Oral drops
One-Alpha (Neon Healthcare Ltd) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Solution for injection
One-Alpha (Neon Healthcare Ltd) HOSPITAL ONLY PRESCRIBING
  alpha tocopherol SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Oral solution
Vedrop (Recordati Rare Diseases UK Ltd) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  alpha tocopheryl acetate SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Chewable tablet
E-Tabs (Ennogen Healthcare International Ltd) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
Ephynal (Imported (Italy)) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Oral suspension
Alpha tocopheryl acetate (Non-proprietary) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Solution for injection
Alpha tocopheryl acetate (Non-proprietary) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  ascorbic acid SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Chewable tablet
Ascorbic acid (Non-proprietary) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
Ascur (Ennogen Healthcare Ltd) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  biotin HOSPITAL ONLY PRESCRIBING
  Solution for injection
Biotin (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  calcitriol HOSPITAL ONLY PRESCRIBING
  Oral solution
Calcitriol (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  colecalciferol SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Chewable tablet
Colecalciferol (Non-proprietary) NON-FORMULARY
Urgent-D (Vega Nutritionals Ltd) NON-FORMULARY
  Orodispersible tablet
Colecalciferol (Non-proprietary) NON-FORMULARY
  Oral solution
Colecalciferol (Non-proprietary) NON-FORMULARY
Aciferol D3 (Rhodes Pharma Ltd) FORMULARY PRODUCT
Baby D (Kora Healthcare) NON-FORMULARY
E-D3 (Ennogen Healthcare Ltd) NON-FORMULARY
InVita D3 (Consilient Health Ltd) FORMULARY PRODUCT
Pro D3 (Synergy Biologics Ltd) NON-FORMULARY
SunVit D3 (SunVit-D3 Ltd) NON-FORMULARY
Thorens (Galen Ltd) FORMULARY PRODUCT
  Oral drops
Colecalciferol (Non-proprietary) NON-FORMULARY
E-D3 (Ennogen Healthcare Ltd) NON-FORMULARY
Fultium-D3 (Internis Pharmaceuticals Ltd) NON-FORMULARY
InVita D3 (Consilient Health Ltd) NON-FORMULARY
Pro D3 (Synergy Biologics Ltd) NON-FORMULARY
SunVit D3 (SunVit-D3 Ltd) NON-FORMULARY
Thorens (Galen Ltd) NON-FORMULARY
  ergocalciferol NON-FORMULARY
  Oral solution
Ergocalciferol (Non-proprietary) NON-FORMULARY
Eciferol (Rhodes Pharma Ltd) NON-FORMULARY
  Solution for injection
Ergocalciferol (Non-proprietary) NON-FORMULARY
  menadiol sodium phosphate SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  phytomenadione SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  pyridoxine hydrochloride SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  riboflavin SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Modified-release tablet
Riboflavin (Non-proprietary) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  thiamine SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Modified-release tablet
Thiamine (Non-proprietary) NON-FORMULARY
  Solution for injection
Thiamine (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  vitamin A NON-FORMULARY
  Oral drops
Vitamin A (Non-proprietary) NON-FORMULARY
  Solution for injection
Vitamin A (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  vitamin B complex SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Oral solution
Vigranon-B (Wallace Manufacturing Chemists Ltd) NON-FORMULARY
  vitamins A and D SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  vitamins A, B group, C and D FORMULARY PRODUCT
  Oral drops
Abidec Multivitamin (Omega Pharma Ltd) FORMULARY PRODUCT
Dalivit (Dendron Brands Ltd) FORMULARY PRODUCT
Nutrition and metabolic disorders / Zinc deficiency
  zinc sulfate SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
Nutrition and metabolic disorders / Fluid and electrolyte imbalances
  disodium hydrogen citrate with glucose, potassium chloride and sodium chloride FORMULARY PRODUCT
  glucose HOSPITAL ONLY PRESCRIBING
  Infusion
Glucose (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  Solution for infusion
Glucose (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  sodium bicarbonate SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Oral solution
Sodium bicarbonate (Non-proprietary) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
Thamicarb (Thame Laboratories Ltd) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Solution for injection
Sodium bicarbonate (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  Infusion
Sodium bicarbonate (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  sodium chloride SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Modified-release tablet
Slow Sodium (Alturix Ltd) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Solution for injection
Sodium chloride (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  Infusion
Sodium chloride (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  Solution for infusion
Sodium chloride (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  Eye drops
Sodium chloride (Non-proprietary) FORMULARY PRODUCT
Nutrition and metabolic disorders / Low blood volume
  albumin solution HOSPITAL ONLY PRESCRIBING
  Solution for infusion
Albumin solution (Non-proprietary) HOSPITAL ONLY PRESCRIBING
Albunorm (Octapharma Ltd) HOSPITAL ONLY PRESCRIBING
Alburex (CSL Behring UK Ltd) HOSPITAL ONLY PRESCRIBING
Zenalb (Bio Products Laboratory Ltd) HOSPITAL ONLY PRESCRIBING
  gelatin HOSPITAL ONLY PRESCRIBING
  Infusion
Gelaspan (B.Braun Medical Ltd) HOSPITAL ONLY PRESCRIBING
Gelofusine (B.Braun Medical Ltd) HOSPITAL ONLY PRESCRIBING
Geloplasma (Fresenius Kabi Ltd) HOSPITAL ONLY PRESCRIBING
Isoplex (Kent Pharma (UK) Ltd) HOSPITAL ONLY PRESCRIBING
Volplex (Kent Pharma (UK) Ltd) HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Hyperphosphataemia
  sevelamer HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Hypophosphataemia
  phosphate SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Infusion
Phosphate (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  Solution for infusion
Phosphate (Non-proprietary) HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Hyperkalaemia
  insulin HOSPITAL ONLY PRESCRIBING NICE TA151
NICE TA943
  Solution for injection
Insulin (Non-proprietary) HOSPITAL ONLY PRESCRIBING
Actrapid (Novo Nordisk Ltd) HOSPITAL ONLY PRESCRIBING
Humulin S (Eli Lilly and Company Ltd) HOSPITAL ONLY PRESCRIBING
Hypurin Porcine Neutral (Wockhardt UK Ltd) HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Hypokalaemia
  potassium chloride SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Modified-release tablet
Potassium chloride (Non-proprietary) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Oral solution
Kay-Cee-L (Geistlich Sons Ltd) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Infusion
Potassium chloride (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  Solution for infusion
Potassium chloride (Non-proprietary) HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Hypomagnesaemia
  magnesium aspartate SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  magnesium glycerophosphate SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Chewable tablet
Magnesium glycerophosphate (Non-proprietary) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
MagnaPhate (Arjun Products Ltd) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
MagnaPhos (TriOn Pharma Ltd) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  Oral solution
LiquaMag GP (Fontus Health Ltd) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
MagnaPhos (TriOn Pharma Ltd) SPECIALIST INITIATED- Primary care to continue with no Shared Care Guidelines
  magnesium sulfate HOSPITAL ONLY PRESCRIBING
  Solution for injection
Magnesium sulfate (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  Solution for infusion
Magnesium sulfate (Non-proprietary) HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Nutrition (intravenous)
  parenteral nutrition supplements
  Solution for infusion
Dipeptiven (Fresenius Kabi Ltd) HOSPITAL ONLY PRESCRIBING
Peditrace (Fresenius Kabi Ltd) HOSPITAL ONLY PRESCRIBING
  Powder for solution for infusion
Solivito N (Fresenius Kabi Ltd) HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Tyrosinaemia type I
  nitisinone HOSPITAL ONLY PRESCRIBING
  Oral suspension
Orfadin (Swedish Orphan Biovitrum Ltd) HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Mucopolysaccharidosis
  galsulfase HOSPITAL ONLY PRESCRIBING
  Solution for infusion
Naglazyme (BioMarin (U.K.) Ltd) HOSPITAL ONLY PRESCRIBING
  idursulfase HOSPITAL ONLY PRESCRIBING
  Solution for infusion
Elaprase (Takeda UK Ltd) HOSPITAL ONLY PRESCRIBING
  laronidase HOSPITAL ONLY PRESCRIBING
  Solution for infusion
Aldurazyme (Sanofi) HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Gaucher's disease
  imiglucerase HOSPITAL ONLY PRESCRIBING
  miglustat HOSPITAL ONLY PRESCRIBING
  velaglucerase alfa HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Niemann-Pick disease
  miglustat HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Acute porphyrias
  haem arginate HOSPITAL ONLY PRESCRIBING
  Solution for infusion
Normosang (Recordati Rare Diseases UK Ltd) HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Carnitine deficiency
  levocarnitine HOSPITAL ONLY PRESCRIBING
  Oral solution
Levocarnitine (Non-proprietary) HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Wilson's disease
  penicillamine HOSPITAL ONLY PRESCRIBING
  trientine HOSPITAL ONLY PRESCRIBING
  zinc acetate HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Fabry's disease
  agalsidase alfa HOSPITAL ONLY PRESCRIBING
  Solution for infusion
Replagal (Takeda UK Ltd) HOSPITAL ONLY PRESCRIBING
  agalsidase beta HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Pompe disease
  alglucosidase alfa HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Homocystinuria
  betaine HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Mitochondrial disorders
  ubidecarenone HOSPITAL ONLY PRESCRIBING
  Chewable tablet
Ubidecarenone (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  Oral drops
Ubidecarenone (Non-proprietary) HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Urea cycle disorders
  arginine HOSPITAL ONLY PRESCRIBING
  Solution for infusion
Arginine (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  carglumic acid HOSPITAL ONLY PRESCRIBING
  citrulline
  Form unstated
Citrulline (Non-proprietary) HOSPITAL ONLY PRESCRIBING
  sodium benzoate HOSPITAL ONLY PRESCRIBING
  sodium dichloroacetate HOSPITAL ONLY PRESCRIBING
  sodium phenylbutyrate HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Nephropathic cystinosis
  mercaptamine HOSPITAL ONLY PRESCRIBING
  Gastro-resistant capsule
Procysbi (Chiesi Ltd) HOSPITAL ONLY PRESCRIBING
  Eye drops
Mercaptamine (Non-proprietary) HOSPITAL ONLY PRESCRIBING
Cystadrops (Recordati Rare Diseases UK Ltd) HOSPITAL ONLY PRESCRIBING
Nutrition and metabolic disorders / Phenylketonuria
  sapropterin dihydrochloride HOSPITAL ONLY PRESCRIBING NICE TA729